ESCLERODERMIA EN PEDIATRIA PDF
Introducción. “Esclerodermia” significa “piel dura”. El término. “esclerodermia localizada” como diagnóstico principal se refiere al hecho de que las. vol número4 Aplicación del Examen Clínico Objetivo Estructurado en la residencia de Pediatría de la Ciudad de Buenos Angiomas venosos y cefalea en . Morfea o esclerodermia localizada juvenil, descripción de caso clínico y actualización. 9. Arkachaisri T, Vilaiyuk S, Li S, O’Neill KM, Pope E, Higgins.
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The case is presented of an pediatra year-old girl who presented with indurated hypopigmented plaques, of linear distribution in the right upper extremity of two years onset, together with papery texture hyperpigmented indurated plaques with whitish areas of thinned skin in right lower extremity, and leg and ankle swelling.
Esclerodermia: No todo es lupus o artritis en reumatología.
Finally, a randomized, double-blind controlled trial, a multicenter consensus statement and long-term follow-up studies have confirmed the important role of methotrexate MTX for the treatment of JLS. Morphea or juvenile localised scleroderma JLS is an autoimmune, inflammatory, chronic, slowly progressive connective tissue disease of unknown cause that preferably affects skin and underlying tissues. New developments have been also reached in the field of outcome measures.
Recent studies, concerning histopathology and clinical associations with other conditions, open new horizons on the etiopathogenesis of scleroderma.
Scleroderma, in its localized and systemic presentation, represents the third most frequent rheumatic condition in childhood after juvenile idiopathic arthritis and systemic lupus erythematosus.
Studies over recent years highlighted the role of imaging as outcome prdiatria for JLS and introduced a severity score for JSSc. The clinical features and diagnostic tests, including histology were compatible with linear and pansclerotic JLS.
Morphea or juvenile localised scleroderma: We report a case of linear and pansclerotic ELJ type, in which there was a 2 year delay in diagnosis, however the response to treatment was positive as expected. Escleroderkia started with immunosuppressive therapy, physiotherapy, and occupational therapy. In juvenile systemic sclerosis JSSca new severity score has been developed and needs to be validated in future trials.
Early diagnosis, appropriate assessment and effective treatment are crucial to improve the long-term outcome.
To pediahria a case of Juvenil Localised scleroderma in an 8-year old girl, contributing to an early diagnosis and treatment. In juvenile localized scleroderma JLSnew techniques such as Doppler and laser Doppler imaging have shown their usefulness for the daily monitoring of the patients.
Morphea; Juvenile localised scleroderma; Autoimmune.